Successful pregnancy and delivery management in a patient with Bernard Soulier Syndrome
Obstetric Medicine, cilt.16, sa.3, ss.203-205, 2023 (ESCI, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 16 Sayı: 3
- Basım Tarihi: 2023
- Doi Numarası: 10.1177/1753495x211067119
- Dergi Adı: Obstetric Medicine
- Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, Academic Search Premier, CINAHL
- Sayfa Sayıları: ss.203-205
- Anahtar Kelimeler: Bernard Soulier syndrome, macrothrombocytopenia, Pregnancy, thrombosis
- Trakya Üniversitesi Adresli: Evet
Özet
Bernard Soulier Syndrome (BSS) is an inherited bleeding disorder characterized by macrothrombocytopenia and absence of ristocetin-induced platelet aggregation. Clinical findings vary from person to person. Most of the patients are diagnosed with muco-cutaneous bleeding such as purpura, epistaxis and gingival bleeding in early childhood. Few pregnant women with BSS are described in the literature. Management of thrombocytopenia during pregnancy and delivery requires a multidisciplinary approach. The family should be warned about the potentially life-threatening bleeding during pregnancy and the delivery and the decision about mode of delivery should be individualised, involving discussion with patient and multidisciplinary team.