Is immunosuppressive and thrombolytic therapy really effective in a patient with intracardiac thrombosis and pulmonary artery aneurysm due to Behçet’s disease?
Archives of Rheumatology, vol.34, no.4, pp.451-456, 2019 (SCI-Expanded, Scopus, TRDizin)
- Publication Type: Article / Article
- Volume: 34 Issue: 4
- Publication Date: 2019
- Doi Number: 10.5606/archrheumatol.2019.7169
- Journal Name: Archives of Rheumatology
- Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus, TR DİZİN (ULAKBİM)
- Page Numbers: pp.451-456
- Keywords: Behçet’s disease, Intracardiac thrombosis, Pulmonary artery aneurysm
- Trakya University Affiliated: Yes
Abstract
Behçet’s disease (BD) is a rare, multisystemic, chronic vasculitic disorder with unknown etiology. Intracardiac thrombus formation and pulmonary artery aneurysm in BD are very rare. The treatment protocol in patients with vascular involvement, particularly those with pulmonary artery aneurysm accompanied by thrombosis, have not been clearly defined. In this article, we report an exceptional case, who had been treated unsuccessfully with a combination of anti-inflammatory/immunosuppressive therapy and thrombolytic agents, to discuss the poor prognosis of pulmonary artery aneurysm accompanying intracardiac thrombosis in juvenile BD.