Oral verapamil effectively suppressed complex ventricular arrhythmias and unmasked U waves in a patient with Andersen-Tawil syndrome


Erdogan O., Aksoy A., TURGUT N., Durusoy E., SAMSA M., ALTUN A.

Journal of Electrocardiology, cilt.41, sa.4, ss.325-328, 2008 (SCI-Expanded, Scopus) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 41 Sayı: 4
  • Basım Tarihi: 2008
  • Doi Numarası: 10.1016/j.jelectrocard.2008.02.023
  • Dergi Adı: Journal of Electrocardiology
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.325-328
  • Anahtar Kelimeler: Andersen-Tawil, Bidirectional VT, Long QT, Sudden death, Therapy, U wave, Verapamil
  • Trakya Üniversitesi Adresli: Evet

Özet

Andersen-Tawil syndrome (ATS) is a rare, heterogeneous, autosomal dominant, or sporadic disorder characterized by the clinical triad of periodic paralysis, dysmorphic features, and ventricular arrhythmias such as bidirectional ventricular tachycardia (BVT). We present a case of an elderly patient with ATS whose symptomatic ventricular arrhythmias including BVT were effectively suppressed by oral verapamil therapy. © 2008 Elsevier Inc. All rights reserved.